Thumbnail image of: Liver, Gallbladder, and Pancreas: Illustration

Biliary Atresia

What is biliary atresia?

Biliary atresia is a blockage in the small tubes (ducts) that carry bile from the liver to the small intestine. Bile is a fluid that helps the body break down the fat in food. Blockage of the ducts can damage the liver. If this disease is not treated, the liver will stop working.

This is a rare, life-threatening condition that can affect babies soon after birth.

What is the cause?

The cause of biliary atresia is not known. Some possible causes may be:

  • The bile ducts do not form properly before birth.
  • A viral infection or problem with the body’s immune system after birth damages the ducts.

What are the symptoms?

Symptoms may include:

  • Yellowing of the skin and eyes (jaundice) after 2 weeks of age that does not go away by 4 weeks of age
  • Dark urine
  • Pale, clay-colored bowel movements
  • Swollen belly

How is it diagnosed?

Biliary atresia is usually diagnosed during the first 2 months of life. Tests may include:

  • Blood and urine tests
  • Tests of bowel movement
  • An ultrasound, which uses sound waves to show pictures of the liver and bile ducts
  • Nuclear scan, which uses a tiny amount of radioactive chemical injected into a vein to show how well bile flows from the liver to the small intestine
  • Liver biopsy, which is the removal of a small sample of tissue for testing

How is it treated?

Biliary atresia can be treated with 2 types of surgery:

  • Kasai procedure: The damaged ducts are removed and replaced with a loop of intestine so the bile can flow from the liver into the intestine.
  • Liver transplant: The baby is given a liver from another baby who has died or part of a liver from an adult.

Even after a successful Kasai procedure, most babies with biliary atresia slowly develop scarring of the liver (cirrhosis) and need a liver transplant by adulthood.

Your child’s healthcare provider may recommend changes in your baby’s diet or vitamin supplements.

How can I take care of my child?

Follow your child’s healthcare provider’s instructions. Ask your provider:

  • How and when you will hear your child’s test results
  • How long it will take for your child to recover
  • How to take care of your child at home
  • What symptoms or problems you should watch for and what to do if your child has them

Make sure you know when your child should come back for a checkup.

Developed by RelayHealth.
Pediatric Advisor 2015.1 published by RelayHealth.
Last modified: 2013-04-12
Last reviewed: 2014-04-25
This content is reviewed periodically and is subject to change as new health information becomes available. The information is intended to inform and educate and is not a replacement for medical evaluation, advice, diagnosis or treatment by a healthcare professional.
Copyright ©1986-2015 McKesson Corporation and/or one of its subsidiaries. All rights reserved.

Patient Portal

myTuftsMed is our new online patient portal that provides you with access to your medical information in one place. MyTuftsMed can be accessed online or from your mobile device providing a convenient way to manage your health care needs from wherever you are.

With myTuftsMed, you can:

  1. View your health information including your medications, test results, scheduled appointments, medical bills even if you have multiple doctors in different locations.
  2. Make appointments at your convenience, complete pre-visit forms and medical questionnaires and find care or an emergency room.
  3. Connect with a doctor no matter where you are.
  4. Keep track of your children’s and family members’ medical care, view upcoming appointments, book visits and review test results.
  5. Check in on family members who need extra help, all from your private account.


Your privacy is important to us. Learn more about ourwebsite privacy policy. X